3-Methyl-2-oxobutanoic acid ( alpha-Ketoisovaleric acid | 2-Oxoisovaleric acid )

产品货号. M19994 CAS No. 759-05-7

COA

Datasheet

HNMR

HPLC

MSDS

Handing Instructions

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产品名称

3-Methyl-2-oxobutanoic acid
注意事项

本公司产品仅用于科研实验，不得用于人体或动物的临床与诊断
产品简述

α-酮异戊酸是一种异常代谢物，由支链氨基酸的不完全分解产生。 α-酮异戊酸是一种神经毒素、酸原和代谢毒素。
产品描述

alpha-Ketoisovaleric acid is an abnormal metabolite that arises from the incomplete breakdown of branched-chain amino acids. alpha-Ketoisovaleric acid is a neurotoxin an acidogen and a metabotoxin. A neurotoxin causes damage to nerve cells and nerve tissues. alpha-Ketoisovaleric acid is a keto-acid which is a subclass of organic acids. Abnormally high levels of organic acids in the blood (organic acidemia) urine (organic aciduria) the brain and other tissues lead to general metabolic acidosis.
体外实验

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体内实验

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同义词

alpha-Ketoisovaleric acid | 2-Oxoisovaleric acid
通路

Others
靶点

Other Targets
受体

Others
研究领域

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适应症

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1.Yudkoff M et al. Brain amino acid requirements and toxicity: the example of leucine. J Nutr. 2005 Jun;135(6 Suppl):1531S-8S.

计算器

产品手册

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